MSUD Nutrition Management Guidelines
First Edition
February 2013, v.1.50
Current version: v.2.0
Updated: August 2016
Feedback/Comments :: View Release Notes
February 2013, v.1.50
Current version: v.2.0
Updated: August 2016
Feedback/Comments :: View Release Notes
- Overview
- Methodology
- Background
- Biochemical Pathway and Nutrition Treatment Rationale
- Nutrition Assessment
- Comparative Standards
- Nutrition Problem Identification
- Nutrition Intervention
- Nutrition Recommendations
- 1. Nutrition interventions during illness, trauma or surgery
- 2. Nutrition management and Branched chain amino acid (BCAA) blood concentrations
- 3. Thiamin supplementation
- 4. Nutrition interventions during pregnancy, at delivery and during the postpartum period
- 5. Nutrition interventions and liver transplantation
- Monitoring and Evaluation
- Resources
- Benefits and Harms of Implementing the Recommendations
- Barriers to Implementation
- Areas for Future Research
- List of Tables
-
Literature Evidence Summary Tables
- T.1 MSUD Phenotypes
- T.2 Laboratory and Clinical Findings for Classical MSUD
- T.3 Nutrient Recommended Intake and Sources in the Dietary Treatment of Well Individuals with MSUD
- T.4 Recommended Daily Nutrient Intakes of BCAA, PRO, ENERGY and Fluids for Infants, Children and Adults with MSUD (when well)
- T.5 Protein Recommendations during Pregnancy for MSUD
- T.6 Nutrition Problem Identification for MSUD based on the International Dietetics and Nutrition Terminology Reference Manual, 3rd Edition
- T.7 Recommendations for the Nutritional Monitoring of Individuals with MSUD
- T.8 Findings from Delphi Survey Round 1
- T.9 Findings from Delphi Survey Round 2
- T.10 Delphi Round 1 - Lab Test Frequency for Medically Stable Individuals
- T.11 Classification of Medical Foods for MSUD
- T.12 Recommended Nutrient Intake for the School-aged Child with MSUD
- T.13 Sample Menu for Case 5.1: school age child with MSUD
MSUD Toolkit Tables- T.14 Recommended Nutrient Intake for Newborn Infant with MSUD
- T.15 Medical Food and Breast Milk Composition for Case 3.1
- T.16 Calculation of Formula Mix to Meet Recommended Intake for Case 3.1: using breast milk
- T.17 Rounded Calculation of Formula Mix to Meet Recommended Intake for Case 3.1: using breast milk
- T.18 Calculation of Formula Mix to Meet Recommended Intake for Case 3.1: using infant formula
- T.19 Recommended Nutrient Intake for Older Infants with MSUD
- T.20 Calculation of Current Nutrient Intake for Case 4.1
- T.21 Introduction of Solids for Case 4.1
- T.22 Sample Menu with Suggested Feeding Schedule for Case 4.1: infant with MSUD starting solids
- T.23 Nutrition Goals During Acute Illness
- T.24 Monitoring During Acute Illness
- References
- Contributors
- Appendix A: Recommendation Rating Definitions
- Appendix B: Terms
- Disclaimer
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Monitoring and Evaluation
Biomarkers to Monitor
Table 7 provides recommendations for the nutritional monitoring of individuals with MSUD.
[[ TABLE #7, Recommendations for the Nutritional Monitoring of Individuals with MSUD]]
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