MSUD Nutrition Management Guidelines
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Click to view the most recent edition (v.2.0, May 2014).
Nutrition Recommendations
Question
Recommendation 5.1
Consider liver transplantation as a viable treatment option for individuals with MSUD.
Strength of Recommendation:
Insufficient Evidence | Consensus | Weak | Fair | Strong |
Recommendation 5.2
Attempt to bring candidates for liver transplant into good metabolic control (prior to surgery) through dietary management of their BCAA.
Strength of Recommendation:
Insufficient Evidence | Consensus | Weak | Fair | Strong |
Recommendation 5.3
Prevent metabolic decompensation In the perioperative period.
Strength of Recommendation:
Insufficient Evidence | Consensus | Weak | Fair | Strong |
Recommendation 5.4
Allow a relaxation of the BCAA-restricted diet and lift precautions for severe metabolic decompensation for individuals with MSUD who have had successful liver transplantation.
Strength of Recommendation:
Insufficient Evidence | Consensus | Weak | Fair | Strong |
Recommendation 5.5
Provide nutritional counseling to assist in dietary transition, and monitor the anthropometric and nutritional status of individuals with MSUD who have had successful liver transplantation.
Strength of Recommendation:
Insufficient Evidence | Consensus | Weak | Fair | Strong |