Nutrition management of individuals with VLCAD often includes restriction of long-chain dietary fat, supplementation with medium chain triglycerides (MCT), and eating at regular intervals. Lack of appropriate nutrition management can place a patient at nutritional risk and may lead to negative outcomes. However, intercurrent illness, stress, injury, or surgery can trigger an acute event leading to complications including hypoglycemia, cardiomyopathy, and rhabdomyolysis, the pathophysiology of which is not well-defined. Therefore, outcomes in individuals with VLCAD is multifactorial and not dependent on nutrition management alone.
Potential harms include:
Implementing the recommendations can potentially: