Management
Guidelines
Portal
PROP Nutrition Management Guidelines
First Edition
March 2017, v.1.2
Updated: September 2017
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Nutrition Intervention
Overview

Nutrition interventions include actions recommended by the metabolic dietitian to address identified nutrition problems and support optimum management of the individual with PROP.

The recommendations in this guideline (see the next section-Nutrition Recommendations) summarize the evidence and consensus on best practices for individuals with PROP in order to:

  1. Meet nutrient needs for growth, development and health maintenance
  2. Provide interventions to achieve optimal nutritional status and maintain metabolic stability
  3. Provide nutrient supplementation or other treatment modalities to improve outcomes 
  4. Utilize monitoring to inform adjustment to the nutrition prescription and care plan
  5. Reduce risk of secondary complications
  6. Support women who may be considering pregnancy.
  7. Support individuals with PROP for whom liver transplantation is a treatment option
  8. Provide appropriate care to individuals undergoing liver transplantation
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