Optimal UCD treatment management requires ongoing assessment of clinical and nutritional status. Outcome measures from dietary history, anthropometrics, and clinical and laboratory assessment ( TABLE #2, Monitoring the Nutritional Management of an Individual with UCD when Well) are used to determine appropriateness of nutrition recommendations.

A thorough medical and social history are also essential for understanding an individual's clinical needs and ability to effectively adhere to nutrition recommendations.

In infants and young children, evaluation includes: weight, length, head circumference, and weight-for-length.

In older children and adults, evaluation includes: weight, height, and body mass index (BMI).

See: http://www.cdc.gov/growthcharts/cdc_charts.htm and http://www.cdc.gov/growthcharts/who_charts.htm

Assessment of nutrition-focused physical findings includes a physical exam, patient interview, and/or medical record data. Special attention to weight and growth status, gastrointestinal symptoms (e.g., constipation, diarrhea, vomiting), and abnormal skin or hair characteristics are important in UCDs.

See: Monitoring Nutritional Management of UCDs. ( TABLE #2, Monitoring the Nutritional Management of an Individual with UCD when Well)

Food and Nutrition-related history includes: assessment of food and nutrient intake, food and nutrient administration, medication and complementary medication use, knowledge/beliefs/attitudes surrounding nutrition, behavior, access to food and food/nutrition related supplies, physical activity and function, and nutritional quality of life.

Special attention to adequacy and effectiveness of the most recent dietary therapy prescription includes typical intake, medical food consumption (type, amount, and nutrient content), and total nutrient intake. Total nutrient intake includes protein, fat, energy, vitamins and minerals, fiber, and fluids.