These nutrition management recommendations for Urea Cycle Disorders encompass therapies that are typically prescribed and monitored by a metabolic medical team. While metabolic dietitians do not independently implement pharmacologic or medical interventions, comprehensive understanding of the full range of management strategies enables dietitians to contribute effectively within multidisciplinary care teams. The metabolic dietitian plays a critical role in ensuring nutritional adequacy, prescribing and tailoring dietary recommendations, monitoring nutritional outcomes, and advocating for patient safety. Ongoing collaboration and clear communication among physicians, metabolic dietitians, and other health care providers are essential to achieving optimal patient care and outcomes.